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Ectopia lentis
Cataract & Refractive Surgery
Key Points
- •Direction of subluxation is diagnostic: Marfan = superotemporal, homocystinuria = inferonasal, Weill-Marchesani = variable with microspherophakia
- •Iridodonesis (iris tremor) and phacodonesis (lens tremor) are the hallmark clinical signs of lens subluxation
- •Echocardiography is mandatory in all cases of bilateral ectopia lentis to rule out Marfan syndrome (aortic root dilatation)
- •In homocystinuria, general anaesthesia is hazardous due to high thromboembolic risk - use local/regional anaesthesia; treat with pyridoxine (B6)
- •Surgical options include pars plana lensectomy + vitrectomy (posterior dislocation) or capsular tension ring for subluxation; IOL options include scleral-fixated, iris-fixated, or glued IOL
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Keep reading Ectopia lentis
17 more sections are included with the Clinical plan.
- Definition
- Epidemiology
- Aetiology and causes
- Pathogenesis
- Classification
- Risk factors and associations